Neurol. praxi. 2020;21(1):64-67 | DOI: 10.36290/neu.2020.028

Primary central nervous system angiitis

MUDr. Lenka Hvizdošová, MUDr. Michaela Kaiserová, Ph.D., MUDr. Andrea Bártková, Ph.D., prof. MUDr. Petr Kaňovský, CSc.
Neurologická klinika FN a LF UP Olomouc

Primary central nervous system angiitis (PACNS) is a rare disease in which aseptic inflammation of the vessels of the brain, spinal cord, and meninges occurs. Due to heterogeneous and non-specific symptoms it is one of the most difficult diseases to diagnose in neurology. In this paper we present a case of a patient with PACNS and summarize current knowledge about diagnostics and treatment possibilities of this disease.

Keywords: primary angiitis of the CNS, vasculitis, headache.

Published: March 30, 2020  Show citation

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Hvizdošová L, Kaiserová M, Bártková A, Kaňovský P. Primary central nervous system angiitis. Neurol. praxi. 2020;21(1):64-67. doi: 10.36290/neu.2020.028.
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    References

    1. Berlit P, Kraemer M. Cerebral vasculitis in adults: what are the steps in order to establish the diagnosis? Red flags and pitfalls. Clin Exp Immunol 2014; 175: 419-424. Go to original source...
    2. Beuker C, Schmidt A, Strunk D, Sporns PB, Wiendl H, Meuth SG, Minnerup J. Primary angiitis of the central nervous system: diagnosis and treatment. Ther Adv Neurol Disord 2018; 11: 1-16. Go to original source...
    3. Boulouis G, de Boysson H, Zuber M, Guillevin L, Meary E, Costalat V, Pagnoux C, Naggara O. Primary Angiitis of the Central Nervous System: Magnetic Resonance Imaging Spectrum of Parenchymal, Meningeal, and Vascular Lesions at Baseline. Stroke 2017; 48: 1248-1255. Go to original source... Go to PubMed...
    4. Byram K, Hajj-Ali RA, Calabrese L. CNS Vasculitis: An Approach to Differential Diagnosis and Management. Curr Rheumatol Rep 2018; 20: 37. Go to original source... Go to PubMed...
    5. Calabrese LH, Dodick DW, Schwedt TJ, Singhal, AB. Narrative review: reversible cerebral vasoconstriction syndromes. Ann Intern Med 2007; 146: 34-44. Go to original source...
    6. Calabrese LH, Duna GF, Lie JT. Vasculitis in the central nervous system. Arthritis Rheum 1997; 40: 1189-1201. Go to original source...
    7. Calabrese LH, Mallek JA. Primary angiitis of the central nervous system. Report of 8 new cases, review of the literature, and proposal for diagnostic criteria. Medicine (Baltimore) 1988; 67: 20-39. Go to original source... Go to PubMed...
    8. Giannini C, Salvarani C, Hunder G, Brown RD. Primary central nervous systém vasculitis: pathology and mechanisms. Acta Neuropathol 2012; 123: 759-772. Go to original source...
    9. Hajj-Ali RA, Calabrese LH. Diagnosis and classification of central nervous systém vasculitis. J Autoimmun 2014; 48-49: 149-152. Go to original source... Go to PubMed...
    10. Hajj-Ali RA, Calabrese LH. Primary angiitis of the central nervous system in adults. In: Ramirez Curtis M, ed. UpToDate. Waltham, Mass.: UpToDate, 2018.
    11. Lie JT. Classification and histopathologic spectrum of central nervous system vasculitis. Neurol Clin 1997; 15(4): 805-819. Go to original source... Go to PubMed...
    12. Limaye K, Samaniego EA, Adams HP Jr. Diagnosis and Treatment of Primary Central Nervous System Angiitis. Curr Treat Options Neurol 2018; 20: 38. Go to original source... Go to PubMed...
    13. Parisi JE, Moore PM. The role of biopsy in vasculitis of the central nervous system. Semin Neurol 1994; 14(4): 341-348. Go to original source...
    14. Salvarani C, Brown RD Jr, Calamia KT, Christianson TJ, Weigand SD, Miller DV, Giannini C, Meschia JF, Huston J 3rd, Hunter GG. Primary central nervous system vasculitis: analysis of 101 patients. Ann Neurol 2007; 62: 442-451. Go to original source... Go to PubMed...
    15. Salvarani C, Brown RD Jr, Christianson TJ, Huston J 3rd, Giannini C, Miller DV, Hunder GG. Adult primary central nervous system vasculitis treatment and course: analysis of one hundred sixty-three patients. Arthritis Rheumatol 2015; 67: 1637-1645. Go to original source...
    16. Tomek A. Vaskulitidy centrálního nervového systému. Neurol. praxi 2015; 16: 6.

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